Introduction / Objetives: Focal fibrocartilaginous dysplasia (FFCD) is a rare, benign disorder that has mainly been reported as a cause of deformity around the knees in young children. First described by Bell in 1985, FFCD is a condition causing unilateral tibia vara, which is characterized by a metaphyseal defect with the local presence of fibrocartilaginous tissue. Recently FFCD has been reported in the femur, humerus, and ulna. FFCD frequently undergoes spontaneous resolution. Material and Methods: The authors report on 4 boys observed in the Orthopedic Clinic of Catania between 2002 and 2006. The age at diagnosis ranged from 14-26 months. The location involved the proximal tibia in all cases that presented with unilateral angular deformities with classical bone defects and surrounding sclerosis in the concavity of the deformity. Old children were otherwise healthy with a walking age at an average of 11 months. The metaphysal-diaphysal mean angle measured 22° (range, 18-27°). All patients were followed clinically and radiographically every 3-6 months. Results: The mean duration of follow-up was 4.5 years, with a range of 1.2-7.5 years. All four cases presented with correction at the last follow-up visit. All of the cases were treated conservatively. No osteotomy was necessary and there was a normal physiologic Levine-Drennan angle. There were two cases with minor leg discrepancies (< 1 cm). Conclusion: In conclusion, conservative treatment is recommended in children with a FFCD with an angle < 30° and should be recommended with long-term follow-up to skeletal maturity.

Focal Fibrocartilaginous Tibial Dysplasia: our experience.

PAVONE, VITO;
2010

Abstract

Introduction / Objetives: Focal fibrocartilaginous dysplasia (FFCD) is a rare, benign disorder that has mainly been reported as a cause of deformity around the knees in young children. First described by Bell in 1985, FFCD is a condition causing unilateral tibia vara, which is characterized by a metaphyseal defect with the local presence of fibrocartilaginous tissue. Recently FFCD has been reported in the femur, humerus, and ulna. FFCD frequently undergoes spontaneous resolution. Material and Methods: The authors report on 4 boys observed in the Orthopedic Clinic of Catania between 2002 and 2006. The age at diagnosis ranged from 14-26 months. The location involved the proximal tibia in all cases that presented with unilateral angular deformities with classical bone defects and surrounding sclerosis in the concavity of the deformity. Old children were otherwise healthy with a walking age at an average of 11 months. The metaphysal-diaphysal mean angle measured 22° (range, 18-27°). All patients were followed clinically and radiographically every 3-6 months. Results: The mean duration of follow-up was 4.5 years, with a range of 1.2-7.5 years. All four cases presented with correction at the last follow-up visit. All of the cases were treated conservatively. No osteotomy was necessary and there was a normal physiologic Levine-Drennan angle. There were two cases with minor leg discrepancies (< 1 cm). Conclusion: In conclusion, conservative treatment is recommended in children with a FFCD with an angle < 30° and should be recommended with long-term follow-up to skeletal maturity.
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/20.500.11769/100789
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